From Wikipedia, the free encyclopedia
Blue rubber bleb nevus syndrome (or "BRBNS", or "blue rubber bleb syndrome, or "blue rubber-bleb nevus", or "Bean syndrome") is a rare disorder that consists mainly of abnormal blood vessels affecting the gastrointestinal tract.
[edit] Presentation
BRBNS is a venous malformation, formerly, though incorrectly, thought to be related to the hemangioma. It carries significant potential for serious or fatal bleeding. Lesions are most commonly found on the skin and in the small intestine and distal large bowel.
[edit] Causes
The causes of this syndrome are unknown. Not more than a few hundred cases have been described worldwide.
[edit] References
- Moodley M, Ramdial P (1993). "Blue rubber bleb nevus syndrome: case report and review of the literature". Pediatrics 92 (1): 160–2. PMID 8516068
- Dobru D, Seuchea N, Dorin M, Careianu V (2004). "Blue rubber bleb nevus syndrome: case report and literature review". Rom J Gastroenterol 13 (3): 237–40. PMID 15470538
- Dwivedi M, Misra SP (2002). "Blue rubber bleb nevus syndrome causing upper GI hemorrhage: a novel management approach and review". Gastrointest Endosc 55 (7): 943–6. doi:10.1067/mge.2002.124212. PMID 12024162
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