Sucrose intolerance

From Wikipedia, the free encyclopedia

Sucrose intolerance Classification and external resources
ICD-10	E74.3
ICD-9	271.3
OMIM	222900
DiseasesDB	29844

Sucrose intolerance, also called Congenital Sucrase-Isomaltase Deficiency (CSID) or Sucrase-isomaltase deficiency , is the condition in which sucrase, an enzyme needed for proper metabolization of sucrose, is not produced in the small intestine. The result of consuming sucrose is excess gas production and often diarrhea and malabsorption.

[edit] See also

• Fructose malabsorption
• Gastroenterology
• Lactose intolerance
• Sucrase-isomaltase

[edit] External links

• http://www.csidinfo.com/
• http://www.orphan-europe.com/sucrase_mangel_gb.html
• http://www.sucraid.net/

v • d • e Digestive system - Digestive disease - Gastroenterology (primarily K20-K93, 530-579) Esophagus Esophagitis - GERD - Achalasia - Boerhaave syndrome - Nutcracker esophagus - Zenker's diverticulum - Mallory-Weiss syndrome - Barrett's esophagus Stomach/ duodenum Peptic (gastric/duodenal) ulcer - Gastritis - Gastroenteritis - Duodenitis - Dyspepsia - Pyloric stenosis - Achlorhydria - Gastroparesis - Gastroptosis - Portal hypertensive gastropathy - Gastric antral vascular ectasia Hernia Inguinal (Indirect, Direct) - Femoral - Umbilical - Incisional - Diaphragmatic - Hiatus Noninfective enteritis & colitis Inflammatory bowel disease (IBD, Crohn's disease, Ulcerative colitis) - noninfective gastroenteritis Other intestinal vascular (Abdominal angina, Mesenteric ischemia, Ischemic colitis, Angiodysplasia) - Ileus/Bowel obstruction (Intussusception, Volvulus) - Diverticulitis/Diverticulosis - Irritable bowel syndrome (IBS) other functional intestinal disorders (Constipation, Diarrhea, Megacolon/Toxic megacolon, Proctalgia fugax) - Anal fissure/Anal fistula - Anal abscess - Rectal prolapse - Proctitis (Radiation proctitis) Liver/hepatitis Alcoholic liver disease - Liver failure (Hepatic encephalopathy, Acute liver failure) - Cirrhosis - PBC - Liver abscess - Autoimmune hepatitis - NASH - Fatty liver - Peliosis hepatis - Hepatic veno-occlusive disease - Portal hypertension - Hepatorenal syndrome Accessory digestive Gallbladder: Gallstones - Choledocholithiasis - Cholecystitis - Cholesterolosis - Rokitansky-Aschoff sinuses Biliary tree: Cholangitis - Cholestasis/Mirizzi's syndrome - PSC - Biliary fistula - Ascending cholangitis Pancreatic: Acute pancreatitis - Chronic pancreatitis - Pancreatic pseudocyst - Hereditary pancreatitis - Exocrine pancreatic insufficiency - Pancreatic fistula Other/general Appendicitis - Peritonitis (Spontaneous bacterial peritonitis) Malabsorption (coeliac, Tropical sprue, Blind loop syndrome, Whipple's) postprocedural: Gastric dumping syndrome - Postcholecystectomy syndrome bleeding: Hematemesis - Melena - Gastrointestinal bleeding (Upper, Lower) See also congenital

v • d • e Inborn error of carbohydrate metabolism (including glycogen storage diseases) (E73-74, 271) Disaccharide catabolism Lactose intolerance - Sucrose intolerance Monosaccharide catabolism fructose: Essential fructosuria - Fructose intolerance galactose/galactosemia : Galactokinase deficiency - Galactose-1-phosphate uridylyltransferase galactosemia - Galactose epimerase deficiency Monosaccharide transport Glucose-galactose malabsorption - Inborn errors of renal tubular transport (Renal glycosuria) Glycolysis GSD type VII, Tarui's, phosphofructokinase - Triosephosphate isomerase deficiency - Pyruvate kinase deficiency Pyruvate catabolism PDHA - Fumarase deficiency Gluconeogenesis PCD - Fructose bisphosphatase deficiency - GSD type I, von Gierke, glucose 6-phosphatase Glycogenesis GSD type 0, glycogen synthase - GSD type IV, Andersen's, branching Glycogenolysis GSD type II, Pompe's, glucosidase - GSD type III, Cori's, debranching - GSD type V, McArdle, glycogen phosphorylase/GSD type VI, Hers', glycogen phosphorylase - GSD type I, von Gierke, glucose 6-phosphatas Pentose phosphate pathway Glucose-6-phosphate dehydrogenase deficiency - Pentosuria Other Hyperoxaluria see also glycolysis enzymes, pentose phosphate pathway enzymes, fructose and galactose metabolism enzymes