Esthesioneuroblastoma

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Esthesioneuroblastoma
Classification and external resources
Esthesioneuroblastoma
ICD-10 C30.0
ICD-9 160.0
ICD-O: M9522/3
OMIM 133450
DiseasesDB 32047
eMedicine med/748 
MeSH D018304

Esthesioneuroblastoma is a form of tumor presenting near the nasal cavity. It can cause loss of vision.[1]

It is often considered synonymous with "olfactory neuroblastoma",[2][3]but the tissue of origin is not yet well characterized.

It was first characterized in 1924.[4][5]

Contents

[edit] Incidence/prevalence

According to the BBC, only 200 cases of the disease have been recorded worldwide in the past two decades.[6]

A 1997 literature search identified 1,457 cases in the published literature.[7]

[edit] Treatment

Several surgical approaches have been described,[8][9][10][11] but post-excision recurrence rates have remained relatively high.

[edit] Notable cases

The disease was brought into prominence by the case of Chantal Sébire, who was suffering from the disease and ended her life after being denied euthanasia.[12]

[edit] See also

[edit] References

  1. ^ Sharma S, Sharma MC, Johnson MH, Lou M, Thakar A, Sarkar C (2007). "Esthesioneuroblastoma - a clinicopathologic study and role of DNA topoisomerase alpha". Pathol. Oncol. Res. 13 (2): 123–9. doi:PAOR.2007.13.2.0123. PMID 17607373. 
  2. ^ e_16/12343800 at Dorland's Medical Dictionary
  3. ^ Medcyclopaedia - Esthesioneuroblastoma. Retrieved on 2008-03-22.
  4. ^ Esthesioneuroblastoma. Retrieved on 2008-03-22.
  5. ^ Berger L, Luc G, Richard D. L'esthésioneuroépithéliome olfactif. Bull Assoc Franç Étude Cancer 1924;13:410-421.
  6. ^ BBC NEWS. Retrieved on 2008-03-22.
  7. ^ Broich G, Pagliari A, Ottaviani F (1997). "Esthesioneuroblastoma: a general review of the cases published since the discovery of the tumour in 1924". Anticancer Res. 17 (4A): 2683-706. PMID 9252701. 
  8. ^ Vergani F, Pirola E, Fiori L, Pagni F, Parmigiani F, Sganzerla EP (2007). "Combined transcranial and endoscopic nasal resection for esthesioneuroblastoma. Technical note". J Neurosurg Sci 51 (2): 99-102. PMID 17571044. 
  9. ^ Unger F, Walch C, Stammberger H, Papaefthymiou G, Haselsberger K, Pendl G (2001). "Olfactory neuroblastoma (esthesioneuroblastoma): report of six cases treated by a novel combination of endoscopic surgery and radiosurgery". Minim Invasive Neurosurg 44 (2): 79-84. doi:10.1055/s-2001-16000. PMID 11487789. 
  10. ^ Cakmak O, Ergin NT, Yilmazer C, Kayaselçuk F, Barutcu O (2002). "Endoscopic removal of esthesioneuroblastoma". Int. J. Pediatr. Otorhinolaryngol. 64 (3): 233-8. PMID 12090952. 
  11. ^ Prasad KC, Kumar A, Prasad SC, Jain D (2007). "Endoscopic-assisted excision of esthesioneuroblastoma". J Craniofac Surg 18 (5): 1034-8. doi:10.1097/scs.0b013e318157264c. PMID 17912077. 
  12. ^ Tumour woman's death not natural BBC 21 March 2008
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Nervous tissue tumors (ICD-O 9350-9589)
Miscellaneous tumors (9350-9379)
Glioma (9380-9489)
Neuroepitheliomatous (9490-9529)
Meningiomas (9530-9539)
Nerve sheath tumor (9540-9579)
see also brain tumors (though not all brain tumors are of nervous tissue)